• Si un dépistage urinaire de la porphyrie est positif, le traitement de la porphyrie aiguë ne
doit pas être retardé.• L'identification et l'évitement des déclencheurs, une alimentation riche …

METHODS: PubMed, EMBASE and ScienceDirect were screened from the inception of the
databases to May 2019 resulting in 872 articles. Our primary outcome was rate of acute …

Background Hormonal changes, prolonged fasting due to vomiting and some medications
used during pregnancy, may cause an acute crisis of porphyria, sometimes unveiling a …

At 1-month follow-up, the patient's nausea had improved, her pain was well controlled with
minimal analgesia, and her blood pressure and plasma sodium levels had normalized. The …

Discussion Acute porphyria is defined by a partial deficiency in the activity of one of the
enzymes of the haem biosynthesis pathway. Exacerbating factors include drugs, fasting …

Porphyria are a group of congenital errors in porphyrin metabolism and in the heme
biosynthetic pathway. Accumulation of porphyrin precursors (delta-aminolaevulinic acid and …

Background Pregnancy in women with acute hepatic porphyria (AHP) has historically been
associated with significant morbidity. Clinical outcomes have been the focus of previous …

Introduction Acute porphyrias are rare disorders of the heme biosynthetic pathway and
present with acute neurovisceral symptoms that can be induced by hormonal changes and …

Challenges in the management of acute intermittent porphyria with recurrent attacks during
pregnancy: A case report - Vassiliou - 2020 - Clinical Case Reports - Wiley Online Library Skip …

Acute intermittent porphyria is one of three severe hepatic porphyrias. Clinical
manifestations include intermittent acute attacks of abdominal pain and neuropathy with an …