[HTML][HTML] A 54-year-old man with hallucinations and hearing loss

C Steriade, SL Shumak, A Feinstein - CMAJ, 2014 - Can Med Assoc
All of the options were worthy of inclusion in the differential diagnosis (e). Susac syndrome,
an autoimmune vasculopathy, is characterized by branch retinal artery occlusions, deafness …

A case of susac syndrome

JL Zande, MU Farooq - The Neurohospitalist, 2015 - ncbi.nlm.nih.gov
A 32-year-woman presented with mild encephalopathy, unsteady gait and instability, history
of bilateral deafness, and bilateral visual changes. Magnetic resonance imaging of the brain …

Good therapeutic response to infliximab in a case of Susac syndrome refractory to immunotherapies including tocilizumab

S Demuth, T Bogdan, L Kremer, L Lanotte… - Journal of …, 2022 - Springer
We report the therapeutic response of a challenging case of advanced Susac syndrome.
The disease began in 2008 at age 23. This male patient presented headaches and transient …

[HTML][HTML] Long-term neuropsychological and psychiatric outcomes in Susac's syndrome

C Bolton, M Lacy - The Journal of Neuropsychiatry and …, 2019 - Am Neuropsych Assoc
To the Editor: Susac's syndrome is a rare, autoimmune angiopathy of unknown etiology. It is
characterized by a clinical triad of branch retinal artery occlusion, encephalopathy, and …

[HTML][HTML] A patient with susac syndrome and bipolar disorder

A Zormann, K Sylle, S Schroller… - The primary care …, 2012 - psychiatrist.com
To the Editor: Susac syndrome is a rare disease first described in 1979 by Susac et al. 1 To
date, more than 200 cases have been published worldwide. 2 The typical clinical …

[CITATION][C] Toward a serum biomarker of disease activity in Susac syndrome

TA Hardy - European Journal of Neurology, 2023 - Wiley Online Library
Susac's syndrome is a brain-eye-ear syndrome in which patients are typically affected by
cognitive impairment due to cerebral microinfarctions with a predilection for the corpus …

Rituximab in the treatment of Susac's syndrome: Report of a case

C Monferrer-Adsuara… - European Journal …, 2021 - journals.sagepub.com
Significance Susac's syndrome is a rare retinocochleocerebral immune-mediated
endotheliopathy and clinically manifests as a pathognomonic triad of encephalopathy …

Susac syndrome: neurologic, psychiatric, ophthalmologic otorhinolaryngologic and neuroradiologic features of a rare autoimmune disease

A Mike, V Gaál, A Németh, F Kövér, S Komoly… - Orvosi hetilap, 2007 - europepmc.org
UNLABELLED: Encephalopathy, recurrent occlusion of retinal arteries and hearing loss
comprise the clinical picture of Susac's syndrome. The correct diagnosis is frequently missed …

Incomplete Susac syndrome exacerbated after natalizumab

L Zhovtis Ryerson, I Kister, M Snuderl… - Neuroimmunology & …, 2015 - AAN Enterprises
A 66-year-old man with hypertension presented with right-sided numbness and slurred
speech. MRI revealed a large left frontoparietal area of T2-weighted hyperintensity with …

Aggressive immunosuppression in Susac's syndrome: 10 years of follow-up

E Capiluppi, L Romano, SV Luccarelli, A Macerollo… - Neurological …, 2018 - Springer
Dear Editor, Susac's syndrome (SS) is a rare disease affecting small vessels of the brain,
inner ear, and retina [1]. The pathophysiology is related to a selective immune mechanism …