The final unique stage in the metabolism of L-isoleucine involves the cleavage of 2-
methylacetoacetyl-CoA to acetyl-CoA and propionyl-CoA (Section 10.4). The propionyl-CoA …

Vitamin B12 (cobalamin) is an essential cofactor of two enzymes, methionine synthase and
methylmalonyl-CoA mutase. The conversion of the vitamin to its coenzymes requires a …

Two infants with lethargy, vomiting, convulsions, coma and marked metabolic acidosis were
found to have very high concentrations of methylmalonic acid in their serum and urine. In …

It has been found that high amounts of aspartate equivalents in combination with vitamin
B12 and/or biotin, especially in relative absence of glutamate equivalents, improve the …

ObjectiveTo review evidence on the associations between vitamin B12 intake and its
biomarkers, vitamin B12 intake and its functional health outcomes, and vitamin B12 …

Sir—In a commentary, B Å Bengtsson (Oct 23), 1 discusses the effects of growth-hormone
therapy in critically ill patients. Growth hormone is an anabolic hormone that spares protein …

I read with interest the case presented by Ntranos et al. of acute-onset bilateral lesions in the
globus pallidi, hearing loss (possible cochlear dysfunction), and upper thoracic anterior …

Группа изобретений относится к медицине и диетическому питанию. Предложены
композиции (варианты) для энтерального применения для лечения и/или …

RESULTS The patient's cells showed 26~ residual activity compared to control lines. This is
in the upper range of previously reported activities for patients with this disorder (Morrow et …