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Pulmonary artery to the left atrium fistula as an unusual cause of cyanosis in the newborn

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Summary

A fistula between the pulmonary artery (PA) and the left atrium (LA) is a rare form of congenital heart disease, 34 cases having been described in the literature, all from the right pulmonary artery (RPA). Only six cases were diagnosed in the newborn period. We report such a case, diagnosed at 1 day of age by Doppler echocardiography, with an unusual site of the fistula.

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Authors and Affiliations

  1. Section of Cardiology, Hôpital du Haut-Levêque, Avenue Magellan, 33604, Pessac-Bordeaux, France

    Maria Jimenez, Anne Fournier & Alain Choussat

  2. Sainte-Justine Hospital, Montreal, Canada

    Maria Jimenez, Anne Fournier & Alain Choussat

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  1. Maria Jimenez
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  2. Anne Fournier
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  3. Alain Choussat
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Jimenez, M., Fournier, A. & Choussat, A. Pulmonary artery to the left atrium fistula as an unusual cause of cyanosis in the newborn. Pediatr Cardiol 10, 216–220 (1989). https://doi.org/10.1007/BF02083296

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