Background: Angioedema without major urticarial flares (hives) is poorly understood. Its
causes are diverse, and little is known about its pathogenic mechanisms. We report on our 11 …

Background Acquired angioedema due to C1-inhibitor deficiency (C1-INH-AAE) is a rare
disease with no prevalence data or approved therapies. Objective To report data on patients …

Background & Aims: Serum cryoglobulins (CGs) are present in patients with chronic hepatitis
C virus (HCV) infection, but their long-term clinical importance has not been established. …

Methods Groups of angioedema patients were as follow: 117 C1-INH-HAE, 32 idiopathic
non-histaminergic (2 hereditary with FXII mutations, 12 hereditary of unknown etiology, 18 …

Abstract 1596 Angioedema with acquired deficiency of C1 inhibitor (C1-INH) is a rare
syndrome associated with B lymphocyte disorders, usually identified as acquired angioedema (…

C1-inhibitor (C1-inh) is a member of serine protease inhibitor (serpin) family which contains
a common tertiary structure composed of three-sheets and several α-helices. Genetic …

Hereditary angioedema-induced acute pancreatitis : clinical picture and effect of C1-esterase
inhibitor replacement IRIS SUrplus Home Sfoglia Macrotipologie & tipologie Autore Titolo …

Background The inherited deficiency of C1‐inhibitor (C1‐ INH ), which can be quantitative (type
I) or qualitative (type II ), is characterized by recurrent attacks of oedema, and it is known …

Methods Case description with clinical assessment and diagnostic tests: C1-INH quantitative/qualitative
tests, C4 serum levels, CT scans of extremities. Results An adopted 45 y-old …

Methods Sixty-nine patients with HAE-FXII coming from 23 families and 196 patients with
HAE-unknown coming from 65 families were studied. Results Pedigree analysis revealed an …